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Primary pulmonary hypertension (AERS syndrome)

It is characterized by myocardial hypertrophy of the right ventricle, expansion of the pulmonary artery. Fibrosis and intima fibroelastosis, fibrinoid-necrotic arteritis of small branches of the pulmonary artery and thrombosis are morphologically detected. It is believed that the direct cause is fibrosis and fibroelastosis of the muscular layer of the pulmonary arterioles, most likely related to a genetically determined defect in smooth muscle fibers. Treats diseases with an autosomal dominant type of inheritance. More common in young women and girls.

Clinical picture. Dyspnea, cyanosis, right ventricular hypertrophy, physical changes in the lungs are usually absent, “drumsticks”.

Severe, rapidly progressing primary pulmonary hypertension, occurring with severe cyanosis, shortness of breath, polycythemia, severe right-sided hypertrophy, is defined as AERSA ​​syndrome.

At X-ray examination, a sharp expansion of the proximal pulmonary artery is determined by weakening the pulmonary pattern in the peripheral parts of the lungs, an increase in the size of the right heart sections, expansion of the roots of the lungs and their enhanced pulsation.

On ECG: signs of a sharp overload of the right ventricle and its hypertrophy.

ECHO KG: expansion of the pulmonary artery, enlargement of the right ventricle, regurgitation of blood into the right ventricle.

Treatment. Calcium antagonists, a-blockers.

Forecast. Adverse; death from progressive right ventricular failure.

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Primary pulmonary hypertension (AERS syndrome)

    John Ross, Jr. (John Ross, Jr.) Primary (or idiopathic) pulmonary hypertension is an infrequent disease, the diagnosis of which is based on the exclusion of other known and more common causes of increased pressure in the pulmonary circulation. In most cases, primary pulmonary hypertension is diagnosed in women aged 20–40 years, which, however, does not exclude
  2. Pulmonary hypertension
    580. DECREASE THE HYPERTENSION OF THE SMALL ROUND OF THE CIRCULATION 1. HEPARIN 2. EUFILLIN 3. NITROGLYCERIN 4. PRE-ISOLONE 5. NORADRENALINE 1) only 1,2,4 is true 2) only 2,3 are true 3 3) only 1,4 are true 4) only 3 are true 5) everything is correct 121 581. FOR PULMONARY HYPERTENSION OF VENOUS TYPE IS NOT CHARACTERISTIC 1) pulmonary capillary pressure of 10 mm Hg. Art. 2) cough, hemoptysis 3)
    PRIMARY PULMONARY HYPERTENSION Primary pulmonary hypertension (PLH) is a disease of unclear etiology, the diagnostic criteria of which are the following signs according to M. Riedel and J. Widimsky (1987): 1. Increased pressure in the pulmonary trunk and normal wedging pressure. 2. The absence of heart and lung diseases. 3. Lack of local anomalies of pulmonary vessels according to
  4. Persistent Pulmonary Hypertension
    Persistent pulmonary hypertension (PLH) in newborns is a disease characterized by severe arterial hypoxemia, resulting from an increase in pulmonary vascular resistance with bypassing blood from the pulmonary arteries into the systemic circulation. This pathology is also known as the persistent fetal circulation syndrome. Etiology. PLG often complicates the course of such
  5. Persistent Pulmonary Hypertension in Newborns
    SYNONYMS Persistent pulmonary hypertension in newborns, persistent fetal circulation. DEFINITION Resistant fetal blood circulation in a newborn (SFKN) is a symptom complex characterized by refractory arterial hypoxemia resulting from persistent high pulmonary vascular resistance and shunting of blood from right to left through the OAP and oval window. CODE
    Pulmonary hypertension (LH) is a pathological syndrome caused by an increase in blood pressure in the pulmonary circulation (ICC). The pressure in the ICC is considered elevated if it exceeds normal values: systolic - 26-30 mm Hg, diastolic 13-19 mm Hg. PH causes severe disorders in vital organs and systems, especially in the lungs and heart. This causes
  8. Primary ciliary dyskinesia (immotile cilia syndrome) and Cartagener's syndrome
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  9. Portal Hypertension Syndrome
    Portal hypertension syndrome is a symptom complex caused by impaired blood circulation in the portal vein system. Leading symptoms: • splenomegaly; • dilatation of the esophagus and anterior abdominal wall; • ascites. Etiology. Causes of portal hypertension are blocks of blood circulation in the portal system. Suprahepatic block - thrombosis of the hepatic veins, inferior vena cava; stenosis and obliteration
    The article "Cardiopulmonary resuscitation in children" is in the section "Emergency conditions in pediatrics", the article "Sudden cardiac death" - in the section "Emergency conditions in diseases of the cardiovascular system." The concept of a “chain of survival” is at the heart of the activities carried out by patients with arrest of blood circulation and respiration. It consists of actions performed sequentially in place.
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    With the development of terminal conditions, the timely and proper conduct of primary cardiopulmonary resuscitation allows, in some cases, to save the lives of children and return the injured to normal activities. Mastering the elements of emergency diagnostics of terminal conditions, solid knowledge of the technique of primary cardiopulmonary resuscitation, extremely clear, “automatic” performance of all
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