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Primary pulmonary hypertension (AERCA syndrome)

It is characterized by myocardial hypertrophy of the right ventricle, extension of the pulmonary artery trunk. Morphologically revealed fibrosis and intestinal fibroelastosis, fibrinoid-necrotic arteritis of small branches of the pulmonary artery and thrombosis. It is believed that the immediate cause is fibrosis and fibroelastosis of the muscle layer of pulmonary arterioles, most likely associated with a genetically conditioned defect of smooth muscle fibers. It refers to diseases with an autosomal dominant type of inheritance. It is more common in young women and girls.

Clinical picture. Shortness of breath, cyanosis, right ventricular hypertrophy, physical changes in the lungs are usually absent, "drum sticks."

Severe, rapidly progressive primary pulmonary hypertension, occurring with a sharp cyanosis, dyspnea, polycythemia, severe right heart hypertrophy is defined as AERSA ​​syndrome.

Radiographic examination determines a sharp expansion of the proximal pulmonary artery with a weakening of the pulmonary pattern in the peripheral parts of the lungs, an increase in the size of the right heart, an expansion of the roots of the lungs, and their enhanced pulsation.

On the ECG: signs of a sharp overload of the right ventricle and its hypertrophy.

ECHO KG: an expansion of the pulmonary artery, an increase in the right ventricle, regurgitation of blood in the right ventricle.

Treatment. Calcium antagonists, a-adrenoblockers.

Forecast. Adverse; death from progressive right ventricular failure.

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Primary pulmonary hypertension (AERCA syndrome)

    John Ross, Jr. Primary (or idiopathic) pulmonary hypertension is a rare disease, the diagnosis of which is based on the exclusion of other known and more common causes of increased pressure in the small circulation. In most cases, primary pulmonary hypertension is diagnosed in women aged 20-40 years, which, however, does not exclude
  2. Pulmonary hypertension
    580. REDUCE THE HYPERTENSION OF A SMALL CIRCLE OF CIRCULATION 1. HEPARIN 2. EVUFILLIN 3. NITROGLYCERINE 4. PREDNISOLONE 5. NORADRENALIN 1) only 1,2,4 is true 2) it is only 2,3) 3) it is true only 1,4 4) only 3 5) All are true 121 581. FOR PULMONARY HYPERTENSION OF THE VENOUS TYPE IS NOT CHARACTERISTIC 1) pulmonary-capillary pressure 10 mm Hg. Art. 2) cough, hemoptysis 3)
    PRIMARY PULMONARY HYPERTENSION Primary pulmonary hypertension (PLG) is a disease of unclear etiology, the criteria for diagnosis of which are the following features according to M. Riedel and J. Widimsky (1987): 1. Increased pressure in the pulmonary trunk and normal seizure pressure. 2. Lack of heart and lung diseases. 3. Absence of local anomalies of pulmonary vessels according to data
  4. Persistent pulmonary hypertension
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  5. Perspirational pulmonary hypertension of newborns
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  8. Primary ciliary dyskinesia (syndrome of immobile cilia) and Kartagener's syndrome
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  9. Syndrome of portal hypertension
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  10. Primary cardiopulmonary resorption
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  11. Primary cardiopulmonary resuscitation
    With the development of terminal conditions, timely and correct primary cardiopulmonary resuscitation allows in some cases to save the life of children and return the victims to normal life. Mastering the elements of emergency diagnosis of terminal conditions, a solid knowledge of the technique of primary cardiopulmonary resuscitation, extremely clear, "automatic" implementation of all
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